Pediatric cancer gene database (Pedican) Home
Pedican
Pediatric cancer database
General information | Literature | Expression | Regulation | Variant | Interaction

Basic Information

Gene ID

2073

Name

ERCC5

Synonym

COFS3|ERCM2|UVDR|XPG|XPGC;excision repair cross-complementing rodent repair deficiency, complementation group 5;ERCC5;excision repair cross-complementing rodent repair deficiency, complementation group 5

Definition

DNA excision repair protein ERCC-5|DNA repair protein complementing XP-G cells|XPG-complementing protein|xeroderma pigmentosum, complementation group G

Position

13q33

Gene Type

protein-coding

Pathways and Diseases

Pathway

Formation of incision complex in GG-NER;PID Reactome;500060

Pathway

Dual incision reaction in GG-NER;PID Reactome;500061

Pathway

DNA Repair;Reactome;REACT:216

Pathway

Formation of transcription-coupled NER (TC-NER) repair complex;PID Reactome;500065

Pathway

Nucleotide excision repair;KEGG PATHWAY;hsa03420

Pathway

Global Genomic NER (GG-NER);PID Reactome;500058

Disease

Sarcoma;FunDO

Disease

Genetic disorders;KEGG DISEASE

Disease

Inherited disorders of DNA repair systems;KEGG DISEASE

Disease

Solid tumor;FunDO

Disease

hypopharyngeal cancer laryngeal cancer;GAD

Disease

Lung cancer;FunDO

Disease

CANCER;GAD

Disease

Cockayne syndrome;FunDO

Disease

Xeroderma pigmentosum, group G;OMIM

Disease

head and neck cancer lung cancer;GAD

Disease

Cerebrooculofacioskeletal syndrome 3;OMIM

Disease

bladder cancer;GAD

Disease

Neoplasms;GAD

Disease

Disorders of nucleotide excision repair;KEGG DISEASE;H00403

External Links

Links to Entrez Gene

2073

Links to all GeneRIF Items

2073

Links to iHOP

2073

Sequence Information

Nucleotide Sequence

>2073 : length: 3561
atgggggtccaggggctctggaagctgctggagtgctccgggcggcaggtcagccccgaa
gcgctggaagggaagatcctggctgttgatattagcatttggttaaaccaagcacttaaa
ggagtccgggatcgccatgggaactcaatagaaaatcctcatcttctcactttgtttcat
cggctctgcaaactcttattttttcgaattcgtcctatttttgtgtttgatggggatgct
ccactattgaagaaacagactttggtgaagagaaggcagagaaaggacttagcgtccagt
gactccaggaaaacgacagagaagcttctgaaaacatttttgaaaagacaagccatcaaa
actgccttcagaagcaaaagagatgaagcactacccagtcttacccaagttcgaagagaa
aacgacctctatgttttgcctcctttacaagaggaagaaaaacacagttcagaagaggaa
gatgaaaaagaatggcaagaaagaatgaatcaaaaacaagcattacaggaagagttcttt
cataatcctcaagcgatagatattgagtctgaggacttcagcagcctgccccctgaagta
aagcatgaaatcttgactgatatgaaagagttcaccaagcgcagaagaacattatttgaa
gcaatgccagaggagtctgatgacttttcacagtaccaactcaaaggcttgcttaaaaag
aactatctgaaccagcatatagaacatgtccaaaaggaaatgaatcagcaacattcagga
cacatccgaaggcagtatgaagatgaagggggctttctgaaggaggtagagtcaaggaga
gtggtctctgaagacacttcacattacatcttgataaaaggtattcaagctaagacagtt
gcagaagtggattcagagtctcttccttcttccagcaaaatgcacggcatgtcttttgac
gtgaagtcatctccatgtgaaaaactgaagacagagaaagagcctgatgctacccctcct
tctccaagaactttactagctatgcaagctgccctgctgggaagtagctcagaagaggag
ctggagagtgaaaatcgaaggcaggcccgtgggaggaacgcacctgctgctgtagacgaa
ggctccatatcaccccggactctttcagccattaagagagctcttgacgatgacgaagat
gtaaaagtgtgtgctggggatgatgtgcagacgggagggccaggagcagaagaaatgcgt
ataaacagctccaccgagaacagtgatgaaggacttaaagtgagagatggaaaaggaata
ccgtttactgcaacacttgcgtcatctagtgtgaactctgcagaggagcacgtagccagc
actaatgaggggagagagcccacagactcagttccaaaagaacaaatgtcacttgttcac
gtggggactgaagcctttccgataagtgatgagtctatgattaaggacagaaaagatcgg
ctgcctctggagagtgcagtggttagacatagtgacgcacctgggctcccgaatggaagg
gaactgacaccggcatctccaacttgtacaaattctgtgtcaaagaatgaaacacatgct
gaagtgcttgagcagcagaacgaactttgcccatatgagagtaaattcgattcttctctt
ctttcaagtgatgatgaaacaaaatgtaaaccgaattctgcttctgaagtcattggccct
gtcagtttgcaagaaacaagtagcatagtaagtgtcccttcagaggcagtagataatgtg
gaaaatgtggtgtcatttaatgctaaagagcatgagaattttctggaaaccatccaagaa
cagcagaccactgaatctgcaggccaggatttaatttccattccaaaggccgtggaacca
atggaaattgactcggaagaaagtgaatctgatggaagtttcattgaagtgcaaagtgtg
attagtgatgaggaacttcaagcagaattccctgaaacttccaaacctccctcagaacaa
ggcgaagaggaactggtaggaactagggagggagaagcccctgctgagtccgagagcctc
ctgagggacaactctgagagggacgacgtggatggtgagccacaggaagctgagaaagat
gcggaagattcgctccatgaatggcaagatattaatttggaggagttggaaactctggag
agcaacctcttagcacagcagaattcactgaaagctcaaaaacagcagcaagaacggatc
gctgctactgtcaccggacagatgttcctggaaagccaggaactcctgcgcctgttcggc
attccctacatccaggctcccatggaagcagaggcgcagtgcgccatcctggacctgact
gatcagacttccggaaccatcactgatgacagtgatatctggctgtttggagcgcggcat
gtctatagaaacttttttaataaaaacaagtttgtagaatattatcaatatgtggacttt
cacaatcaattgggattggaccggaataagttaataaatttggcttatttgcttggaagt
gattataccgaaggaataccaactgtgggttgtgtaaccgccatggaaattctcaatgaa
ttccctgggcatggcctggaacctctcctaaaattctcagaatggtggcatgaagctcaa
aaaaatccaaagataagacctaatcctcatgacaccaaagtgaaaaaaaaattacggaca
ttgcaactcacccctggctttcctaacccagctgttgccgaggcctacctcaaacccgtg
gtggatgactcgaagggatcctttctgtgggggaaacctgatctcgacaaaattagagaa
ttttgtcagcggtatttcggctggaacagaacgaagacagatgaatctctgtttcctgta
ttaaagcaactcgatgcccagcagacacagctccgaattgattccttctttagattagca
caacaggagaaagaagatgctaaacgtattaagagccagagactaaacagagctgtgaca
tgtatgctaaggaaagagaaagaagcagcagccagcgaaatagaagcagtttctgttgcc
atggagaaagaatttgagctacttgataaggcaaaacgaaaaacccagaagagaggcata
acaaataccttagaagagtcatcaagcctgaaaagaaagaggctttcagattctaaacga
aagaatacatgcggtggatttttgggggagacctgcctctcagaatcatctgatggatct
tcaagtgaagatgctgaaagttcatctttaatgaatgtacaaaggagaacagctgcgaaa
gagccaaaaaccagtgcttcagattcgcagaactcagtgaaggaagctcccgtgaagaat
ggaggtgcgaccaccagcagctctagtgatagtgatgacgatggagggaaagagaagatg
gtcctcgtgaccgccagatctgtgtttgggaagaaaagaaggaaactaagacgtgcgagg
ggaagaaaaaggaaaacctaa

Protein Sequence

>2073 : length: 1186
MGVQGLWKLLECSGRQVSPEALEGKILAVDISIWLNQALKGVRDRHGNSIENPHLLTLFH
RLCKLLFFRIRPIFVFDGDAPLLKKQTLVKRRQRKDLASSDSRKTTEKLLKTFLKRQAIK
TAFRSKRDEALPSLTQVRRENDLYVLPPLQEEEKHSSEEEDEKEWQERMNQKQALQEEFF
HNPQAIDIESEDFSSLPPEVKHEILTDMKEFTKRRRTLFEAMPEESDDFSQYQLKGLLKK
NYLNQHIEHVQKEMNQQHSGHIRRQYEDEGGFLKEVESRRVVSEDTSHYILIKGIQAKTV
AEVDSESLPSSSKMHGMSFDVKSSPCEKLKTEKEPDATPPSPRTLLAMQAALLGSSSEEE
LESENRRQARGRNAPAAVDEGSISPRTLSAIKRALDDDEDVKVCAGDDVQTGGPGAEEMR
INSSTENSDEGLKVRDGKGIPFTATLASSSVNSAEEHVASTNEGREPTDSVPKEQMSLVH
VGTEAFPISDESMIKDRKDRLPLESAVVRHSDAPGLPNGRELTPASPTCTNSVSKNETHA
EVLEQQNELCPYESKFDSSLLSSDDETKCKPNSASEVIGPVSLQETSSIVSVPSEAVDNV
ENVVSFNAKEHENFLETIQEQQTTESAGQDLISIPKAVEPMEIDSEESESDGSFIEVQSV
ISDEELQAEFPETSKPPSEQGEEELVGTREGEAPAESESLLRDNSERDDVDGEPQEAEKD
AEDSLHEWQDINLEELETLESNLLAQQNSLKAQKQQQERIAATVTGQMFLESQELLRLFG
IPYIQAPMEAEAQCAILDLTDQTSGTITDDSDIWLFGARHVYRNFFNKNKFVEYYQYVDF
HNQLGLDRNKLINLAYLLGSDYTEGIPTVGCVTAMEILNEFPGHGLEPLLKFSEWWHEAQ
KNPKIRPNPHDTKVKKKLRTLQLTPGFPNPAVAEAYLKPVVDDSKGSFLWGKPDLDKIRE
FCQRYFGWNRTKTDESLFPVLKQLDAQQTQLRIDSFFRLAQQEKEDAKRIKSQRLNRAVT
CMLRKEKEAAASEIEAVSVAMEKEFELLDKAKRKTQKRGITNTLEESSSLKRKRLSDSKR
KNTCGGFLGETCLSESSDGSSSEDAESSSLMNVQRRTAAKEPKTSASDSQNSVKEAPVKN
GGATTSSSSDSDDDGGKEKMVLVTARSVFGKKRRKLRRARGRKRKT



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