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Pediatric cancer database
General information | Literature | Expression | Regulation | Variant | Interaction

Basic Information

Gene ID

6608

Name

SMO

Synonymous

FZD11|Gx|SMOH;smoothened, frizzled family receptor;SMO;smoothened, frizzled family receptor

Definition

frizzled family member 11|protein Gx|seven transmembrane helix receptor|smoothened homolog|smoothened, seven transmembrane spanning receptor

Position

7q32.3

Gene Type

protein-coding

Gene Mutation:

PCGP germline mutation
PCGP somatic mutation
COSMIC somatic mutation

PCGP germline mutation   [Top]

There is no record for SMO

PCGP somatic mutation   [Top]

There is no record for SMO

COSMIC somatic mutation   [Top]

Mutation (CDS; AA; Chr)

Site

Histology

c.1604G>T; p.W535L; 7:128637577-128637577

meningesmeningioma; meningothelial

c.1234C>T; p.L412F;

meningesmeningioma; meningothelial

c.2177G>A; p.R726Q; 7:128639341-128639341

stomachcarcinoma; intestinal_adenocarcinoma

c.983G>A; p.G328D;

large_intestinecarcinoma; adenocarcinoma

c.1417G>C; p.D473H; 7:128636425-128636425

central_nervous_system; brainprimitive_neuroectodermal_tumour-medulloblastoma

c.47_48insGCT; p.L23_G24insL; 7:128616275-128616276

stomachcarcinoma; diffuse_adenocarcinoma

c.1604G>T; p.W535L; 7:128637577-128637577

skincarcinoma; basal_cell_carcinoma

c.868C>A; p.R290S; 7:128632807-128632807

lungcarcinoma; adenocarcinoma

c.1234C>T; p.L412F;

meningesmeningioma; transitional

c.2177G>A; p.R726Q; 7:128639341-128639341

stomachcarcinoma; intestinal_adenocarcinoma

c.1640G>A; p.R547H; 7:128637613-128637613

stomachcarcinoma; intestinal_adenocarcinoma

c.1721C>G; p.S574C;

lungcarcinoma; small_cell_carcinoma

c.47_48insGCT; p.L23_G24insL; 7:128616275-128616276

stomachcarcinoma; mixed_intestinal_and_diffuse_adenocarcinoma-unclassifiable

c.69_70insCTG; p.L23_G24insL;

pleuramesothelioma; biphasic

c.1514C>G; p.P505R;

lungcarcinoma; small_cell_carcinoma

c.1345A>T; p.M449L;

lungcarcinoma; small_cell_carcinoma

c.2287C>T; p.R763*;

large_intestine; coloncarcinoma; adenocarcinoma

c.704C>T; p.A235V;

large_intestine; coloncarcinoma; adenocarcinoma

c.970G>A; p.A324T; 7:128633276-128633276

large_intestine; coloncarcinoma; adenocarcinoma

c.1458C>A; p.D486E;

large_intestine; coloncarcinoma; adenocarcinoma

c.1802C>T; p.A601V;

pancreascarcinoma

c.1604G>T; p.W535L; 7:128637577-128637577

skin; facecarcinoma; basal_cell_carcinoma

c.1604G>T; p.W535L; 7:128637577-128637577

skin; facecarcinoma; basal_cell_carcinoma

c.1604G>T; p.W535L; 7:128637577-128637577

upper_aerodigestive_tract; mouthcarcinoma; basal_cell_carcinoma

c.595C>T; p.R199W; 7:128632337-128632337

skin; facecarcinoma; basal_cell_carcinoma

c.1598G>A; p.S533N; 7:128637571-128637571

central_nervous_system; cerebellumprimitive_neuroectodermal_tumour-medulloblastoma; desmoplastic

c.1604G>T; p.W535L; 7:128637577-128637577

skincarcinoma; basal_cell_carcinoma

c.1604G>T; p.W535L; 7:128637577-128637577

skincarcinoma; basal_cell_carcinoma

c.1685G>A; p.R562Q; 7:128638074-128638074

skincarcinoma; basal_cell_carcinoma

c.1604G>T; p.W535L; 7:128637577-128637577

skin; facecarcinoma; basal_cell_carcinoma

c.1604G>T; p.W535L; 7:128637577-128637577

skin; facecarcinoma; basal_cell_carcinoma

c.1604G>T; p.W535L; 7:128637577-128637577

upper_aerodigestive_tract; mouthcarcinoma; basal_cell_carcinoma

c.595C>T; p.R199W; 7:128632337-128632337

skin; facecarcinoma; basal_cell_carcinoma

c.203_204CC>TT; p.A68V; 7:128616431-128616432

skin; facecarcinoma; basal_cell_carcinoma

c.1046_1047CC>TT; p.T349I; 7:128633352-128633353

skin; facecarcinoma; basal_cell_carcinoma

c.1452_1453CC>TT; p.R485W; 7:128636460-128636461

skin; facecarcinoma; basal_cell_carcinoma

c.1542_1543CC>TT; p.L515F; 7:128637515-128637516

skincarcinoma; basal_cell_carcinoma

c.2263_2264CC>TT; p.P755F; 7:128639427-128639428

skincarcinoma; basal_cell_carcinoma

c.1955C>T; p.A652V; 7:128639119-128639119

skin; facecarcinoma; basal_cell_carcinoma

c.234_235CC>TT; p.(=); 7:128616462-128616463

skincarcinoma; basal_cell_carcinoma

c.1604G>T; p.W535L; 7:128637577-128637577

skin; armcarcinoma; basal_cell_carcinoma

c.1724A>T; p.K575M; 7:128638113-128638113

livercarcinoma; hepatocellular_carcinoma

c.1823A>G; p.N608S;

kidneycarcinoma; renal_cell_carcinoma

c.1203G>C; p.A401A; 7:128633603-128633603

large_intestine; coloncarcinoma; adenocarcinoma

c.1918A>G; p.T640A; 7:128638829-128638829

large_intestine; coloncarcinoma; adenocarcinoma

c.1918A>G; p.T640A; 7:128638829-128638829

large_intestine; coloncarcinoma; adenocarcinoma

c.1169G>A; p.C390Y;

oesophaguscarcinoma; adenocarcinoma

c.2336A>G; p.E779G;

oesophaguscarcinoma; adenocarcinoma

c.1652+4G>T; p.?;

livercarcinoma; hepatocellular_carcinoma

c.1691A>G; p.K564R;

livercarcinoma; hepatocellular_carcinoma

c.1210G>A; p.V404M; 7:128633610-128633610

large_intestine; coloncarcinoma

c.1210G>A; p.V404M; 7:128633610-128633610

large_intestine; coloncarcinoma; adenocarcinoma

c.1210G>A; p.V404M; 7:128633610-128633610

large_intestine; coloncarcinoma; adenocarcinoma

c.1918A>G; p.T640A; 7:128638829-128638829

large_intestine; coloncarcinoma

c.1918A>G; p.T640A; 7:128638829-128638829

large_intestine; coloncarcinoma; adenocarcinoma

c.1918A>G; p.T640A; 7:128638829-128638829

large_intestine; coloncarcinoma; adenocarcinoma

c.350G>T; p.R117L;

upper_aerodigestive_tract; larynxcarcinoma; squamous_cell_carcinoma

c.1802C>T; p.A601V;

pancreascarcinoma; ductal_carcinoma

c.1234C>T; p.L412F;

central_nervous_system; brainprimitive_neuroectodermal_tumour-medulloblastoma; desmoplastic

c.734C>G; p.T245R;

pancreasother; adenoma

c.69_70insCTG; p.L23_G24insL;

pleuramesothelioma

c.628G>A; p.V210M;

lungcarcinoma; adenocarcinoma

c.1549G>T; p.V517L;

lungcarcinoma; adenocarcinoma

c.1263A>T; p.R421R;

lungcarcinoma; adenocarcinoma

c.849C>A; p.A283A;

lungcarcinoma; adenocarcinoma

c.1516G>A; p.D506N;

lungcarcinoma; adenocarcinoma

c.970G>A; p.A324T; 7:128633276-128633276

large_intestine; coloncarcinoma; adenocarcinoma

c.970G>A; p.A324T; 7:128633276-128633276

large_intestine; coloncarcinoma; adenocarcinoma

c.48_49insCTGCTG; p.L23_G24insLL; 7:128616276-128616277

large_intestine; coloncarcinoma; adenocarcinoma

c.1234C>T; p.L412F;

central_nervous_system; brainprimitive_neuroectodermal_tumour-medulloblastoma

c.970G>A; p.A324T; 7:128633276-128633276

biliary_tract; bile_ductcarcinoma

c.1604G>T; p.W535L; 7:128637577-128637577

meningesmeningioma; meningothelial

c.1234C>T; p.L412F;

meningesmeningioma

c.1234C>T; p.L412F;

meningesmeningioma

c.?; p.P647S;

meningesmeningioma

c.1604G>T; p.W535L; 7:128637577-128637577

meningesmeningioma

c.1234C>T; p.L412F;

meningesmeningioma

c.?; p.L522V;

meningesmeningioma

c.1234C>T; p.L412F;

meningesmeningioma

c.1234C>T; p.L412F;

meningesmeningioma

c.1234C>T; p.L412F;

meningesmeningioma

c.?; p.R113Q;

meningesmeningioma

c.1234C>T; p.L412F;

meningesmeningioma

c.1732G>A; p.E578K;

prostatecarcinoma

c.49C>T; p.L17L; 7:128616277-128616277

central_nervous_system; brainglioma; astrocytoma_Grade_IV

c.49C>T; p.L17L; 7:128616277-128616277

central_nervous_system; brainglioma; astrocytoma_Grade_IV

c.1514C>T; p.P505L;

central_nervous_system; brainglioma; astrocytoma_Grade_IV

c.1241T>C; p.V414A;

lungcarcinoma; adenocarcinoma

c.936G>T; p.L312L;

ovarycarcinoma; serous_carcinoma

c.1351C>A; p.R451S;

lungcarcinoma; adenocarcinoma

c.625G>T; p.D209Y;

lungcarcinoma; squamous_cell_carcinoma

c.1640G>T; p.R547L;

lungcarcinoma; adenocarcinoma

c.1924G>T; p.V642L;

lungcarcinoma; adenocarcinoma

c.1922C>G; p.P641R;

lung; right_upper_lobecarcinoma; adenocarcinoma

c.1085T>G; p.L362R;

lungcarcinoma; adenocarcinoma

c.517C>A; p.R173S;

lung; right_upper_lobecarcinoma; adenocarcinoma

c.1901C>T; p.P634L;

lung; right_upper_lobecarcinoma; adenocarcinoma

c.1397C>A; p.T466N;

lung; right_upper_lobecarcinoma; adenocarcinoma

c.1191C>A; p.Y397*;

lung; right_upper_lobecarcinoma; adenocarcinoma

c.1665G>A; p.Q555Q;

breastcarcinoma

c.756C>T; p.F252F;

endometriumcarcinoma; endometrioid_carcinoma

c.790G>T; p.A264S;

large_intestine; coloncarcinoma; adenocarcinoma

c.1724A>G; p.K575R;

large_intestine; caecumcarcinoma; adenocarcinoma

c.1302C>T; p.P434P;

large_intestine; coloncarcinoma; adenocarcinoma

c.879C>T; p.I293I;

large_intestine; coloncarcinoma; adenocarcinoma

c.2160A>C; p.G720G;

large_intestine; coloncarcinoma; adenocarcinoma

c.1597A>G; p.S533G;

large_intestine; rectumcarcinoma; adenocarcinoma

c.2076delC; p.P694fs*82;

large_intestine; rectumcarcinoma; adenocarcinoma

c.1084C>T; p.L362L;

large_intestine; rectumcarcinoma; adenocarcinoma

c.907C>A; p.L303I;

endometriumcarcinoma; endometrioid_carcinoma

c.1470T>A; p.C490*;

endometriumcarcinoma; endometrioid_carcinoma

c.639C>T; p.C213C;

endometriumcarcinoma; endometrioid_carcinoma

c.2107C>T; p.R703*;

endometriumcarcinoma; endometrioid_carcinoma

c.2168A>T; p.D723V;

endometriumcarcinoma; endometrioid_carcinoma

c.2260G>A; p.A754T;

endometriumcarcinoma; endometrioid_carcinoma

c.1684C>T; p.R562W;

endometriumcarcinoma; endometrioid_carcinoma

c.1905G>T; p.Q635H;

endometriumcarcinoma; endometrioid_carcinoma

c.1597A>G; p.S533G;

large_intestine; coloncarcinoma; adenocarcinoma

c.1203G>T; p.A401A;

large_intestine; coloncarcinoma; adenocarcinoma

c.868C>A; p.R290S; 7:128632807-128632807

large_intestine; caecumcarcinoma; adenocarcinoma

c.2076delC; p.P694fs*82;

large_intestine; caecumcarcinoma; adenocarcinoma

c.2057C>T; p.A686V;

kidneycarcinoma; clear_cell_renal_cell_carcinoma

c.1352G>A; p.R451H;

endometriumcarcinoma; endometrioid_carcinoma

c.1446C>T; p.R482R;

endometriumcarcinoma; endometrioid_carcinoma

c.1315G>A; p.E439K;

breastcarcinoma

c.703G>A; p.A235T;

kidneycarcinoma; clear_cell_renal_cell_carcinoma

c.2302C>T; p.P768S;

breastcarcinoma

c.2097T>G; p.S699R;

kidneycarcinoma; clear_cell_renal_cell_carcinoma

c.2076delC; p.P694fs*82;

large_intestine; coloncarcinoma; adenocarcinoma

c.1686G>A; p.R562R;

large_intestine; coloncarcinoma; adenocarcinoma

c.1843T>C; p.S615P;

large_intestine; coloncarcinoma; adenocarcinoma

c.1685G>A; p.R562Q; 7:128638074-128638074

large_intestine; coloncarcinoma; adenocarcinoma

c.1419C>T; p.D473D;

large_intestine; coloncarcinoma; adenocarcinoma

c.1796C>A; p.P599H;

urinary_tract; bladdercarcinoma

c.1623G>A; p.T541T;

endometriumcarcinoma; endometrioid_carcinoma

c.2051C>T; p.P684L;

endometriumcarcinoma; endometrioid_carcinoma

c.734C>T; p.T245M;

large_intestine; coloncarcinoma; adenocarcinoma

c.1210G>A; p.V404M; 7:128633610-128633610

large_intestine; coloncarcinoma; adenocarcinoma

c.1045A>C; p.T349P;

breastcarcinoma

c.596G>A; p.R199Q;

large_intestine; coloncarcinoma; adenocarcinoma

c.838G>T; p.G280C;

urinary_tract; bladdercarcinoma

c.869G>A; p.R290H;

skinmalignant_melanoma

c.799C>T; p.L267F;

skin; mucosalmalignant_melanoma

c.442C>T; p.Q148*;

skin; scalpcarcinoma; squamous_cell_carcinoma


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