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Pediatric cancer database
General information | Literature | Expression | Regulation | Variant | Interaction

Basic Information

Gene ID

5077

Name

PAX3

Synonymous

CDHS|HUP2|WS1|WS3;paired box 3;PAX3;paired box 3

Definition

paired box homeotic gene 3|paired box protein Pax-3|paired domain gene 3|paired domain gene HuP2

Position

2q35-q37|2q35

Gene Type

protein-coding

Gene Mutation:

PCGP germline mutation
PCGP somatic mutation
COSMIC somatic mutation

PCGP germline mutation   [Top]

There is no record for PAX3

PCGP somatic mutation   [Top]

Variant (Variant; Chr; Position)

Genotype (MutationType; MutationClass; ReferenceAllele; Genotype; Origin)

Disease (CancerType; ValidationStatus; SequencingType)

PAX3_E10_UTR_3; chr2; 223065258

SUB; UTR_3; C; C/T; SOMATICMB; VALID; WGS

COSMIC somatic mutation   [Top]

Mutation (CDS; AA; Chr)

Site

Histology

c.1385C>T; p.P462L;

large_intestine; coloncarcinoma; adenocarcinoma

c.467G>A; p.R156H;

large_intestine; coloncarcinoma; adenocarcinoma

c.396A>C; p.E132D;

large_intestine; coloncarcinoma; adenocarcinoma

c.1451+1G>A; p.?;

skin; abdomenmalignant_melanoma

c.1388T>A; p.V463D;

pancreascarcinoma

c.808C>T; p.R270C;

prostatecarcinoma; adenocarcinoma

c.1507C>G; p.L503V;

livercarcinoma; hepatocellular_carcinoma

c.1122G>A; p.S374S;

upper_aerodigestive_tract; pharynxcarcinoma; squamous_cell_carcinoma

c.1388T>A; p.V463D;

pancreascarcinoma; ductal_carcinoma

c.189C>A; p.A63A;

lungcarcinoma; adenocarcinoma

c.1071C>A; p.P357P;

lungcarcinoma; adenocarcinoma

c.597C>T; p.P199P;

lungcarcinoma; adenocarcinoma

c.844C>G; p.Q282E;

lungcarcinoma; adenocarcinoma

c.1465C>T; p.L489F;

skin; extremitymalignant_melanoma

c.177C>T; p.I59I;

pancreascarcinoma; ductal_carcinoma

c.867C>G; p.L289L;

NSNS

c.1045G>T; p.D349Y;

lungcarcinoma; small_cell_carcinoma

c.707G>A; p.R236H; 2:222805126-222805126

ovarycarcinoma; serous_carcinoma

c.1090T>G; p.S364A; 2:222793186-222793186

ovarycarcinoma; serous_carcinoma

c.933T>C; p.S311S;

lungcarcinoma; squamous_cell_carcinoma

c.821G>T; p.W274L;

lungcarcinoma; squamous_cell_carcinoma

c.375C>G; p.N125K; 2:222868567-222868567

ovarycarcinoma; serous_carcinoma

c.1061A>T; p.Y354F; 2:222793215-222793215

ovarycarcinoma; serous_carcinoma

c.1442C>A; p.P481Q;

lungcarcinoma; squamous_cell_carcinoma

c.381C>A; p.G127G;

lung; middle_lobecarcinoma; adenocarcinoma

c.912G>C; p.T304T;

lungcarcinoma; squamous_cell_carcinoma

c.1093A>T; p.S365C;

lungcarcinoma; squamous_cell_carcinoma

c.1232C>A; p.A411E;

lungcarcinoma; squamous_cell_carcinoma

c.1127C>A; p.P376H;

lungcarcinoma; adenocarcinoma

c.1462A>G; p.I488V;

breastcarcinoma

c.1450G>A; p.A484T;

endometriumcarcinoma; endometrioid_carcinoma

c.447G>A; p.P149P;

large_intestine; caecumcarcinoma; adenocarcinoma

c.565G>A; p.D189N;

large_intestine; caecumcarcinoma; adenocarcinoma

c.998C>T; p.P333L;

large_intestine; coloncarcinoma; adenocarcinoma

c.373A>G; p.N125D;

large_intestine; caecumcarcinoma; adenocarcinoma

c.1271C>T; p.T424M;

large_intestine; coloncarcinoma; adenocarcinoma

c.442G>A; p.V148M;

large_intestine; coloncarcinoma; adenocarcinoma

c.1230C>T; p.Y410Y;

large_intestine; coloncarcinoma; adenocarcinoma

c.1271C>T; p.T424M;

large_intestine; coloncarcinoma; adenocarcinoma

c.981C>T; p.T327T;

large_intestine; caecumcarcinoma; adenocarcinoma

c.879delG; p.F294fs*87;

large_intestine; coloncarcinoma; adenocarcinoma

c.719G>T; p.R240I;

large_intestine; coloncarcinoma; adenocarcinoma

c.1230C>T; p.Y410Y;

large_intestine; coloncarcinoma; adenocarcinoma

c.195C>T; p.H65H;

large_intestine; coloncarcinoma; adenocarcinoma

c.110G>A; p.R37H;

large_intestine; coloncarcinoma; adenocarcinoma

c.806A>G; p.N269S;

large_intestine; coloncarcinoma; adenocarcinoma

c.812G>A; p.R271H;

large_intestine; coloncarcinoma; adenocarcinoma

c.1060T>C; p.Y354H;

large_intestine; caecumcarcinoma; adenocarcinoma

c.1028C>T; p.T343M;

large_intestine; rectumcarcinoma; adenocarcinoma

c.202C>T; p.R68W;

large_intestine; rectumcarcinoma; adenocarcinoma

c.1075A>C; p.T359P;

endometriumcarcinoma; endometrioid_carcinoma

c.720A>G; p.R240R;

endometriumcarcinoma; endometrioid_carcinoma

c.659G>A; p.R220H;

endometriumcarcinoma; endometrioid_carcinoma

c.1361G>T; p.S454I;

endometriumcarcinoma; endometrioid_carcinoma

c.1087T>A; p.F363I;

endometriumcarcinoma; endometrioid_carcinoma

c.1230C>T; p.Y410Y;

endometriumcarcinoma; endometrioid_carcinoma

c.1215G>A; p.Q405Q;

endometriumcarcinoma; endometrioid_carcinoma

c.1275G>T; p.V425V;

kidneycarcinoma; clear_cell_renal_cell_carcinoma

c.688C>A; p.Q230K;

endometriumcarcinoma; endometrioid_carcinoma

c.373A>G; p.N125D;

large_intestine; coloncarcinoma; adenocarcinoma

c.230G>A; p.R77H;

large_intestine; caecumcarcinoma; adenocarcinoma

c.433C>T; p.R145*;

large_intestine; coloncarcinoma; adenocarcinoma

c.247G>A; p.V83I;

endometriumcarcinoma; endometrioid_carcinoma

c.829C>T; p.Q277*;

large_intestine; caecumcarcinoma; adenocarcinoma

c.590C>T; p.S197L;

urinary_tract; bladdercarcinoma

c.1091C>A; p.S364Y;

large_intestine; coloncarcinoma; adenocarcinoma

c.18C>T; p.G6G;

large_intestine; rectumcarcinoma; adenocarcinoma

c.707G>A; p.R236H; 2:222805126-222805126

large_intestine; rectumcarcinoma; adenocarcinoma

c.374A>G; p.N125S;

large_intestine; coloncarcinoma; adenocarcinoma

c.1249G>A; p.G417R;

large_intestine; caecumcarcinoma; adenocarcinoma

c.1459C>G; p.Q487E;

urinary_tract; bladdercarcinoma

c.785G>A; p.R262Q;

large_intestine; coloncarcinoma; adenocarcinoma

c.1413T>C; p.Y471Y;

large_intestine; caecumcarcinoma; adenocarcinoma

c.836G>A; p.G279E;

urinary_tract; bladdercarcinoma

c.1366A>G; p.T456A;

kidneycarcinoma; clear_cell_renal_cell_carcinoma

c.658C>T; p.R220C;

stomachadenocarcinoma


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