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Pediatric cancer database
General information | Literature | Expression | Regulation | Variant | Interaction

Basic Information

Gene ID

4864

Name

NPC1

Synonymous

NPC;Niemann-Pick disease, type C1;NPC1;Niemann-Pick disease, type C1

Definition

Niemann-Pick C1 protein

Position

18q11-q12

Gene Type

protein-coding

Gene Mutation:

PCGP germline mutation
PCGP somatic mutation
COSMIC somatic mutation

PCGP germline mutation   [Top]

There is no record for NPC1

PCGP somatic mutation   [Top]

There is no record for NPC1

COSMIC somatic mutation   [Top]

Mutation (CDS; AA; Chr)

Site

Histology

c.2710G>A; p.G904R;

NSmalignant_melanoma

c.2710G>A; p.G904R;

NSmalignant_melanoma

c.3776A>G; p.K1259R;

salivary_glandcarcinoma; adenoid_cystic_carcinoma

c.482G>T; p.R161L;

lungcarcinoma; small_cell_carcinoma

c.685G>A; p.E229K;

large_intestine; coloncarcinoma; adenocarcinoma

c.142C>T; p.P48S;

large_intestine; coloncarcinoma; adenocarcinoma

c.2525T>C; p.F842S;

large_intestine; coloncarcinoma; adenocarcinoma

c.856G>A; p.A286T;

large_intestine; coloncarcinoma; adenocarcinoma

c.925A>G; p.I309V;

livercarcinoma

c.3337A>C; p.T1113P;

livercarcinoma

c.1027G>A; p.G343R;

large_intestine; rectumadenoma

c.3216C>T; p.N1072N;

NSNS

c.3216C>T; p.N1072N;

NSNS

c.3216C>T; p.N1072N;

NSNS

c.3216C>T; p.N1072N;

NSNS

c.3216C>T; p.N1072N;

NSNS

c.3321C>T; p.G1107G;

oesophaguscarcinoma; adenocarcinoma

c.1396G>A; p.D466N;

oesophagus; lower_thirdcarcinoma; adenocarcinoma

c.1605T>C; p.G535G;

oesophaguscarcinoma; adenocarcinoma

c.612C>T; p.T204T;

stomachcarcinoma; adenocarcinoma

c.3265G>A; p.E1089K;

livercarcinoma

c.61T>C; p.F21L;

large_intestine; coloncarcinoma; adenocarcinoma

c.3797G>A; p.R1266Q;

livercarcinoma

c.1947+8G>C; p.?;

large_intestine; coloncarcinoma

c.3701T>C; p.L1234S;

large_intestine; coloncarcinoma

c.3175C>T; p.R1059*;

large_intestine; coloncarcinoma

c.2727C>T; p.C909C;

kidneycarcinoma; clear_cell_renal_cell_carcinoma

c.816G>A; p.M272I;

haematopoietic_and_lymphoid_tissuelymphoid_neoplasm; follicular_lymphoma

c.814A>T; p.M272L;

haematopoietic_and_lymphoid_tissuelymphoid_neoplasm; follicular_lymphoma

c.336A>T; p.T112T;

lungcarcinoma; adenocarcinoma

c.1261C>T; p.Q421*;

lungcarcinoma; adenocarcinoma

c.934_935insT; p.S312fs*3;

pancreascarcinoma; ductal_carcinoma

c.287G>A; p.R96K;

livercarcinoma

c.1358T>G; p.I453S;

lungcarcinoma; small_cell_carcinoma

c.1009C>T; p.R337W;

autonomic_ganglianeuroblastoma

c.2993T>G; p.F998C; 18:19372552-19372552

ovarycarcinoma; serous_carcinoma

c.2292G>T; p.A764A; 18:19375349-19375349

ovarycarcinoma; serous_carcinoma

c.2427C>T; p.S809S;

ovarycarcinoma; serous_carcinoma

c.3591C>T; p.S1197S;

ovarycarcinoma; serous_carcinoma

c.1795C>G; p.L599V;

lungcarcinoma; squamous_cell_carcinoma

c.828C>T; p.Y276Y;

lungcarcinoma; adenocarcinoma

c.2692G>T; p.D898Y;

lungcarcinoma; adenocarcinoma

c.2229T>A; p.T743T;

lungcarcinoma; squamous_cell_carcinoma

c.3378C>G; p.I1126M;

lungcarcinoma; squamous_cell_carcinoma

c.1010_1011GG>TT; p.R337L;

lung; right_upper_lobecarcinoma; adenocarcinoma

c.3730C>A; p.L1244I;

lung; right_upper_lobecarcinoma; adenocarcinoma

c.3493G>A; p.V1165M;

breastcarcinoma

c.2409T>C; p.G803G;

large_intestine; coloncarcinoma; adenocarcinoma

c.864delT; p.F288fs*22;

large_intestine; coloncarcinoma; adenocarcinoma

c.782C>T; p.T261M;

large_intestine; coloncarcinoma; adenocarcinoma

c.3522G>A; p.A1174A;

breastcarcinoma

c.2918A>T; p.D973V;

breastcarcinoma

c.2780C>T; p.A927V;

large_intestine; coloncarcinoma; adenocarcinoma

c.1820G>A; p.R607Q;

large_intestine; coloncarcinoma; adenocarcinoma

c.3535A>G; p.M1179V;

large_intestine; coloncarcinoma; adenocarcinoma

c.3452C>T; p.A1151V;

large_intestine; coloncarcinoma; adenocarcinoma

c.3621delT; p.F1207fs*35;

large_intestine; coloncarcinoma; adenocarcinoma

c.482G>A; p.R161Q;

large_intestine; coloncarcinoma; adenocarcinoma

c.2820G>A; p.S940S;

large_intestine; colonNS

c.1351G>A; p.E451K;

large_intestine; coloncarcinoma; adenocarcinoma

c.2990G>A; p.R997K;

large_intestine; coloncarcinoma; adenocarcinoma

c.3778A>C; p.S1260R;

large_intestine; coloncarcinoma; adenocarcinoma

c.2355A>C; p.L785F;

large_intestine; coloncarcinoma; adenocarcinoma

c.984C>T; p.S328S;

large_intestine; coloncarcinoma; adenocarcinoma

c.3307G>A; p.G1103S;

haematopoietic_and_lymphoid_tissuehaematopoietic_neoplasm; acute_myeloid_leukaemia

c.2395_2396insT; p.C799fs*7;

large_intestine; coloncarcinoma; adenocarcinoma

c.1351G>A; p.E451K;

large_intestine; rectumcarcinoma; adenocarcinoma

c.1773G>T; p.V591V;

large_intestine; rectumcarcinoma; adenocarcinoma

c.1756G>C; p.E586Q;

breastcarcinoma

c.1298C>A; p.P433H;

endometriumcarcinoma; endometrioid_carcinoma

c.834G>A; p.A278A;

endometriumcarcinoma; endometrioid_carcinoma

c.2477C>A; p.S826Y;

endometriumcarcinoma; endometrioid_carcinoma

c.706G>T; p.A236S;

endometriumcarcinoma; endometrioid_carcinoma

c.2713C>T; p.Q905*;

large_intestine; caecumcarcinoma; adenocarcinoma

c.414A>C; p.K138N;

endometriumcarcinoma; endometrioid_carcinoma

c.358T>G; p.F120V;

endometriumcarcinoma; endometrioid_carcinoma

c.1350C>A; p.I450I;

endometriumcarcinoma; endometrioid_carcinoma

c.2292G>A; p.A764A;

large_intestine; caecumcarcinoma; adenocarcinoma

c.258C>T; p.N86N;

large_intestine; coloncarcinoma; adenocarcinoma

c.865G>T; p.A289S;

kidneycarcinoma; clear_cell_renal_cell_carcinoma

c.1955C>T; p.S652L;

endometriumcarcinoma; endometrioid_carcinoma

c.1948-2A>G; p.?;

endometriumcarcinoma; endometrioid_carcinoma

c.1003T>A; p.L335M;

breastcarcinoma

c.1533G>A; p.T511T;

endometriumcarcinoma; endometrioid_carcinoma

c.3617A>C; p.K1206T;

endometriumcarcinoma; endometrioid_carcinoma

c.3208G>A; p.G1070S;

endometriumcarcinoma; endometrioid_carcinoma

c.1989C>A; p.I663I;

endometriumcarcinoma; endometrioid_carcinoma

c.2559G>C; p.L853L;

urinary_tract; bladdercarcinoma

c.2811C>T; p.F937F;

breastcarcinoma

c.3199G>A; p.E1067K;

large_intestine; coloncarcinoma; adenocarcinoma

c.2380C>T; p.R794W;

large_intestine; coloncarcinoma; adenocarcinoma

c.515C>A; p.A172D;

kidneycarcinoma; clear_cell_renal_cell_carcinoma

c.514G>A; p.A172T;

kidneycarcinoma; clear_cell_renal_cell_carcinoma

c.2432A>G; p.Q811R;

large_intestine; caecumcarcinoma; adenocarcinoma

c.2286_2287delCT; p.F763fs*8;

large_intestine; coloncarcinoma; adenocarcinoma

c.1521C>T; p.A507A;

large_intestine; coloncarcinoma; adenocarcinoma

c.901G>A; p.E301K;

kidneycarcinoma; clear_cell_renal_cell_carcinoma

c.208A>G; p.N70D;

endometriumcarcinoma; endometrioid_carcinoma

c.1863C>A; p.V621V;

endometriumcarcinoma; endometrioid_carcinoma

c.2730C>T; p.G910G;

large_intestine; coloncarcinoma; adenocarcinoma

c.761C>T; p.P254L;

breastcarcinoma

c.315G>A; p.L105L;

urinary_tract; bladdercarcinoma

c.1431G>A; p.T477T;

cervixcarcinoma; squamous_cell_carcinoma

c.2793C>T; p.N931N;

breastcarcinoma

c.1038C>T; p.C346C;

large_intestine; caecumcarcinoma; adenocarcinoma

c.2291C>T; p.A764V;

large_intestine; rectumcarcinoma; adenocarcinoma

c.2841C>T; p.F947F;

urinary_tract; bladdercarcinoma

c.2802A>G; p.R934R;

large_intestine; caecumcarcinoma; adenocarcinoma

c.526C>A; p.L176M;

skinmalignant_melanoma

c.1210C>T; p.R404W;

skinmalignant_melanoma

c.2012C>T; p.S671F;

skinmalignant_melanoma

c.2579T>C; p.L860S;

skin; neckmalignant_melanoma

c.2017G>A; p.G673S;

skinmalignant_melanoma

c.3626G>A; p.G1209E;

kidneycarcinoma; clear_cell_renal_cell_carcinoma


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