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Pedican
Pediatric cancer database
General information | Literature | Expression | Regulation | Variant | Interaction

Basic Information

Gene ID

1736

Name

DKC1

Synonymous

CBF5|DKC|DKCX|NAP57|NOLA4|XAP101;dyskeratosis congenita 1, dyskerin;DKC1;dyskeratosis congenita 1, dyskerin

Definition

CBF5 homolog|H/ACA ribonucleoprotein complex subunit 4|cbf5p homolog|nopp140-associated protein of 57 kDa|nucleolar protein NAP57|nucleolar protein family A member 4|snoRNP protein DKC1

Position

Xq28

Gene Type

protein-coding

Gene Mutation:

PCGP germline mutation
PCGP somatic mutation
COSMIC somatic mutation

PCGP germline mutation   [Top]

There is no record for DKC1

PCGP somatic mutation   [Top]

There is no record for DKC1

COSMIC somatic mutation   [Top]

Mutation (CDS; AA; Chr)

Site

Histology

c.1498A>T; p.K500*;

livercarcinoma

c.850C>T; p.R284*;

haematopoietic_and_lymphoid_tissue; tonsillymphoid_neoplasm; diffuse_large_B_cell_lymphoma

c.1498A>T; p.K500*;

livercarcinoma

c.971A>G; p.E324G;

livercarcinoma

c.583C>T; p.R195*;

central_nervous_system; brainglioma; oligodendroglioma_Grade_III

c.548G>A; p.R183Q;

central_nervous_system; brainglioma; oligodendroglioma_Grade_III

c.358C>A; p.H120N;

large_intestine; colonadenoma

c.634A>T; p.R212*;

breastcarcinoma

c.309T>C; p.H103H;

lungcarcinoma; small_cell_carcinoma

c.217G>T; p.A73S;

autonomic_ganglianeuroblastoma

c.1036G>A; p.A346T;

lungcarcinoma; adenocarcinoma

c.762G>C; p.M254I;

lung; right_lower_lobecarcinoma; adenocarcinoma

c.121G>T; p.E41*;

lung; middle_lobecarcinoma; adenocarcinoma

c.210A>G; p.T70T;

lung; right_upper_lobecarcinoma; adenocarcinoma

c.857T>C; p.V286A;

lung; right_upper_lobecarcinoma; adenocarcinoma

c.763A>G; p.S255G;

large_intestine; coloncarcinoma; adenocarcinoma

c.1393T>C; p.L465L;

large_intestine; coloncarcinoma; adenocarcinoma

c.210A>G; p.T70T;

large_intestine; coloncarcinoma; adenocarcinoma

c.216T>C; p.L72L;

large_intestine; coloncarcinoma; adenocarcinoma

c.1331C>T; p.T444I;

large_intestine; rectumcarcinoma; adenocarcinoma

c.1297A>C; p.K433Q;

endometriumcarcinoma; endometrioid_carcinoma

c.1494G>T; p.K498N;

endometriumcarcinoma; endometrioid_carcinoma

c.58A>G; p.K20E;

breastcarcinoma

c.1354G>A; p.E452K;

breastcarcinoma

c.39T>G; p.H13Q;

breastcarcinoma

c.1492_1494delAAG; p.K505delK;

large_intestine; caecumcarcinoma; adenocarcinoma

c.329G>A; p.R110Q;

endometriumcarcinoma; endometrioid_carcinoma

c.797T>C; p.V266A;

endometriumcarcinoma; endometrioid_carcinoma

c.404G>A; p.C135Y;

endometriumcarcinoma; endometrioid_carcinoma

c.660T>C; p.C220C;

endometriumcarcinoma; endometrioid_carcinoma

c.1418G>T; p.S473I;

endometriumcarcinoma; endometrioid_carcinoma

c.1118G>T; p.R373I;

endometriumcarcinoma; endometrioid_carcinoma

c.422G>A; p.R141H;

endometriumcarcinoma; endometrioid_carcinoma

c.1317C>T; p.A439A;

large_intestine; coloncarcinoma; adenocarcinoma

c.1334C>T; p.A445V;

large_intestine; caecumcarcinoma; adenocarcinoma

c.55C>T; p.R19W;

large_intestine; coloncarcinoma; adenocarcinoma

c.90A>G; p.I30M;

endometriumcarcinoma; endometrioid_carcinoma

c.1305G>A; p.P435P;

endometriumcarcinoma; endometrioid_carcinoma

c.493G>T; p.G165W;

endometriumcarcinoma; endometrioid_carcinoma

c.324G>C; p.W108C;

prostatecarcinoma; adenocarcinoma

c.622G>A; p.D208N;

skinmalignant_melanoma


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